ʻO ke ʻano paipu koʻikoʻi loa ka ʻawa bile no kā mākou ʻōnaehana digestive. Hoʻopili ia i ka pilina ma waena o ʻekolu mau mea ʻokoʻa, me ka ate, ka ʻōpū, a me ka ʻōpū. Hoʻohele kēia paipu liʻiliʻi i ka wai bile mai ke ake a i ka gallbladder. I ka lilo ʻana o nā cell i mea ʻino i loko o ke kahawai bile duct, alakaʻi ia i ka maʻi maʻi bile duct i nā maʻi. He maʻi maʻi kakaʻikahi a paʻakikī, ʻaʻole hiki ke ho'ōla maʻalahi. Hiki i kēia pilikia ke pili iā ʻoe i kēlā me kēia makahiki a ʻoi aku ka nui ma luna o 50 mau makahiki. Aia nā ʻano lāʻau lapaʻau like ʻole no ka mālama ʻana i ka maʻi maʻi bile duct, kahi ʻoi ka koho maikaʻi loa no nā maʻi. Inā ʻaʻole kōkua kēia koho, hiki i ke kauka ke hana lāʻau lapaʻau chemotherapy a i ʻole ka lāʻau lapaʻau. Hoʻomaopopo pū ʻia kahi ʻano hoʻololi o ke ake no ka mālama ʻana i kēia maʻi olakino.
Nā ʻano o ka maʻi maʻi ʻawaʻawa bile
ʻEkolu mau ʻano like ʻole kēia maʻi olakino. Penei keia:
- Intrahepatic Cholangiocarcinoma: Loaʻa ia ma nā ʻāpana like ʻole o ka ʻawa bile i loko o ke ake. ʻAʻole maʻamau kēia pilikia a manaʻo pinepine ʻia he maʻi maʻi ate.
- Cholangiocarcinoma maʻamau: Hoʻoulu pinepine ʻia kahi maʻi maʻi bile duct ma waho o ke ake. He kakaikahi kēia pilikia a hiki ke hoʻopilikia i ka 20 a i ʻole 30 pakeneka o nā kānaka.
- Perihilar Cholangiocarcinoma: Loaʻa ia ma ka hui hema a me ka ʻākau o kahi auwai bile. Pili kēia pilikia i ka 50 a i ʻole 60 pakeneka o nā kānaka, a ua like kona mau hōʻailona me ka cholangiocarcinoma distal.
Nā hōʻailona o ka maʻi maʻi maʻi bile
ʻO nā hōʻailona o kēia pilikia olakino penei:
- ʻO Nausea a me ka Vomiting
- ʻO ka'ōmā pouli
- ʻO nā moena ʻulaʻula
- ʻO Jaundice
- ʻO kaʻehaʻeha
- ʻO ka pohō kaumahaʻole
- 'Oloke
- Fiva a me nā anuanu
- ʻO ka ʻōpū ʻōpū
- ʻO Pruritus
- ʻO ka hopena maikaʻi
ʻIke ʻia o ka maʻi maʻi ʻawaʻawa bile
ʻO nā hoʻokolohua diagnostics no kēia kūlana olakino penei:
- Endoscopic Ultrasound: An endoscopy ua hui pū ʻia me kahi ultrasound e kiʻi i nā kiʻi mai ka ʻōpū o ka ʻōpū. Ua like kēia kaʻina hana me ka endoscopy kiʻekiʻe a ʻoi aku ka maikaʻi o ka hoʻopaʻa ʻana i ka maʻi maʻi bile duct i nā maʻi.
- angiography: Hoʻohana ke kauka i kēia kaʻina hana no ka loiloi ʻana i ka hoʻopaʻa ʻia ʻana o ka duct bile a me ka ʻike ʻana i nā kīʻaha koko a puni ka ʻōpū.
- ʻO ka Endoscopy o ka gastrointestinal: Hoʻokomo ʻia kahi mea hana liʻiliʻi a maʻalahi, i kapa ʻia ʻo endoscope, i loko o ka esophagus ma o ka waha a i ʻole ka puʻu. Hoʻopili ʻia me kahi kāmela no ka nānā ʻana i ka ʻōnaehana digestive. I loko o kēia ʻoki ʻana, pono paha ka mea maʻi i ke kumuhana anesthetic a i ʻole lāʻau ʻeha.
- Endoscopic Retrograde Cholangiography: Hoʻokomo ke kauka kūikawā i kahi mea ʻokoʻa i loko o ka ʻawa bile ma o ka endoscope. Hiki iā ia ke lawe i nā kiʻi X-ray e hōʻike i nā mea ʻino e pili ana Ka maʻi 'aʻai. I loko o kēia kaʻina hana, hiki ke hana ʻia kahi hoʻāʻo biopsy no ka ʻike ʻana i kahi kiko bile duct.
- Percutaneous Transhepatic Cholangiography: Hoʻopili ʻia kahi nila liʻiliʻi me kekahi o nā auwai bile a hoʻokomo ʻia kahi mea ʻokoʻa ma o kēia hāmeʻa. Ma hope o ka hoʻokahe ʻana, lawe paha ke kauka i nā kiʻi X-ray e nānā i ka lāʻau biliary. ʻOi aku ka maikaʻi o kēia kaʻina hana ma mua o ka ERCP no ka mea e ʻae ia i ke komo pololei ʻana i kahi duct bile.
- Cholangioscopy: Hoʻokomo ʻia kahi mea endoscopic kūikawā, ʻike ʻia ʻo cholangioscopy i loko o ka ʻawa bile, kahi e hiki ai i ke kauka ke nānā maʻalahi i ka ʻōpū. E hana ʻia kēia kaʻina hana diagnostic i ka wā o kahi ʻoki ERCP.
Nā Koho Lapaʻau ʻana i ka maʻi maʻi maʻi bile
Hiki ke mālama 'ia ka ma'i 'a'ai bile ma nā 'ano he nui. Aia kēia mau mea i lalo:
- ʻAla: Hoʻopili ia i ka wehe piha ʻana a i ʻole ka ʻāpana bile. Hoʻomaopopo pū ʻia kēia ala lapaʻau no ka hoʻokele ʻana i kahi duct block.
- Kemoterapi: Hoʻohana ʻia nā lāʻau lapaʻau ikaika no ka luku ʻana i nā maʻi maʻi a i ʻole ka hōʻemi ʻana i nā maʻi maʻi. Hiki iā lākou ke hoʻokomo i loko o kahi vein a hele a puni ke kino. Hana ʻia kēia kaʻina hana ma mua o ka hoʻololi ʻana i ke akepaʻa. He mea kōkua ia no ka cholangiocarcinoma holomua e kōkua i ka hoʻolohi i ka maʻi a hoʻomaha i kona mau hōʻailona a me nā hōʻailona.
- Immunotherapy: Ke hoʻohana nei ke kauka i nā mea hoʻopaneʻe mākaʻikaʻi, e kōkua ana i ka ʻōnaehana pale e hakakā me nā maʻi maʻi maʻi. He kūpono kēia ʻano lapaʻau no ka maʻi maʻi bile duct kiʻekiʻe, ke hiki ʻole i nā ʻenehana ʻē aʻe ke mālama i kēia pilikia olakino.
- Lapaʻau Radiation: Hoʻohana ʻia nā kukuna ikehu kiʻekiʻe no ka pale ʻana i nā maʻi kanesa. Hoʻopili ia i kahi mīkini kahi e kuhikuhi ʻia ai ka radiation i ka ʻōpū. Hoʻohana kekahi mea mālama ola i nā pahu liʻiliʻi o ka radiation, hiki ke hoʻokomo ʻia i loko o nā kīʻaha koko. Kōkua kēia ʻokiʻoki i ka hōʻemi ʻana i nā maʻi koko a hāʻawi i ka pale mai kēia kūlana olakino.
- ʻAuwai Biliary: Hoʻokomo ʻia kahi paipu lahilahi i loko o ka pā bile e hoʻokahe i ka wai bile maikaʻi ʻole. Kōkua kēia i ka hoʻopau ʻana i ke keʻakeʻa ʻana o kēia auwai a hoʻēmi i nā hōʻailona e like me ka jaundice, ka ʻili, a me nā mea hou aku.
